Treatment of Encephalotrigeminal Angiomatosis (Sturge-Weber Disease) by Hemispherectomy
نویسندگان
چکیده
منابع مشابه
Treatment of encephalotrigeminal angiomatosis (Sturge-Weber disease) by hemispherectomy.
Encephalotrigeminal angiomatosis or SturgeWeber's disease is an uncommon congenital disorder which can vary greatly in the extent of its manifestations, but which in severe cases can lead to infantile hemiplegia associated with fits, behavioural disorders and mental backwardness. Until comparatively recently specific therapy was largely limited to anticonvulsant drugs. Only a few isolated repor...
متن کاملSturge-Weber-Dimitri disease: role of hemispherectomy in prognosis.
We report 12 patients with Sturge-Weber-Dimitri disease treated surgically between January 1975 and December 1987. Hemispherectomy was performed on ten, two others underwent occipital lobectomy for intractable seizures. All operations were performed between the ages of 3 months and 20 months, except in two at age 8 and 9 years. The onset of seizures in all was between 2 and 8 months of age, exc...
متن کاملSeizure recurrence 29 years after hemispherectomy for Sturge Weber syndrome.
associated with venous angiomatosis of the leptomeninges and ipsilateral, cutaneous facial port-wine stain (facial angiomatosis). Seizures are seen in more than 80% of cases, cognitive impairment in 50% and frequently glaucoma.1-2 Seizures are the result of leptomeningeal angioma and underlying calcifications. These abnormalities are usually considered to be limited to one hemisphere. Frequentl...
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A case report of rare congenital disease of encephalo-trigeminal angiomatosis (Sturge-Weber Syndrome) (SWS), is presented to alert the anesthesiologist of its potential risk. The case was anesthetized for emergency orthopedic surgery. Anesthesia management is directed towards observing the clinical manifestations of localized superficial skin lesions, extensive systemic involvement, evaluating ...
متن کاملProphylactic antiepileptic treatment in Sturge–Weber disease
PURPOSE In Sturge-Weber disease, motor and cognitive defects are supposed to result mostly from severe epilepsy. They might, therefore be partly prevented by prophylactic antiepileptic drug treatment. This condition constitutes a possible model for the study of prophylactic drug treatment in severe epilepsy. In the present study, we compared the outcome of patients treated prospectively with ph...
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ژورنال
عنوان ژورنال: Archives of Disease in Childhood
سال: 1960
ISSN: 0003-9888,1468-2044
DOI: 10.1136/adc.35.183.433